Rambusch E G, Musholt P, Weissenborn K, Kiehl P, Deicher H
Abteilung Gastroenterologie und Hepatologie, Medizinische Hochschule Hannover.
Z Rheumatol. 1996 Jan-Feb;55(1):58-62.
We describe a patient with livedo racemosa generalisata (LRG), Raynaud's phenomenon, multifocal recurring transitory and complete ischemic attacks and laboratory findings of systemic inflammation. Working diagnoses were vasculitis, mixed connective tissue disease, or Sneddon's syndrome, but echocardiography revealed a left atrial myxoma. Special staining of skin biopsies with alcian-blue showed arterial occlusion caused by myxomatous material. Arterial embolism by parts of the myxoma is suggested to be the cause of the LRG and probably the neurological findings.
我们描述了一名患有全身性网状青斑(LRG)、雷诺现象、多灶性复发性短暂性完全缺血性发作以及系统性炎症实验室检查结果的患者。初步诊断为血管炎、混合性结缔组织病或斯内登综合征,但超声心动图显示左心房黏液瘤。皮肤活检用阿尔辛蓝进行特殊染色显示黏液瘤物质导致动脉闭塞。提示黏液瘤部分导致的动脉栓塞是LRG以及可能是神经学表现的原因。