Oğuzkurt P, Senocak M E, Akçören Z, Kale G, Hiçsönmez A
Department of Pediatric Surgery, Hacettepe University Faculty of Medicine, Ankara, Turkey.
Eur J Pediatr Surg. 1996 Aug;6(4):235-7. doi: 10.1055/s-2008-1066517.
Muscle cell tumors are very uncommon in the spleen as they are in ataxia-telangiectasia. The increased frequency of chromosome breaks probably because of a defect in DNA repair favors the development of benign or malignant tumors in the patient. A case of leiomyoma of the spleen in an 8-year-old boy with ataxia-telangiectasia is reported. The literature on the splenic masses and the localization of leiomyoma is reviewed.
肌肉细胞瘤在脾脏中非常罕见,就如同它们在共济失调-毛细血管扩张症中一样。染色体断裂频率的增加可能是由于DNA修复缺陷,这有利于患者体内良性或恶性肿瘤的发展。本文报道了一例患有共济失调-毛细血管扩张症的8岁男孩的脾脏平滑肌瘤病例。并对有关脾脏肿块和平滑肌瘤定位的文献进行了综述。