Ozkutlu S, Günal N, Cağlar M, Alehan D, Güngör C
Department of Pediatric Cardiology, Hacettepe University, Faculty of Medicine, Samanpazari, Ankara, Turkey.
Int J Cardiol. 1996 Oct 11;56(2):125-9. doi: 10.1016/0167-5273(96)02747-7.
In this report we present two cases with unguarded tricuspid orifice, and review the literature. The complete absence of tricuspid valvular structures is a very rare anomaly coexisting with pulmonary atresia and intact ventricular septum, and is termed unguarded tricuspid orifice. Double tricuspid orifices and isolated dextrocardia were distinguishing features of our first case. The second patient of this report, a 5-year-old boy, is the first case in the literature with this malformation of the tricuspid valve as an isolated anomaly, in addition to being the first surviving case in the literature.
在本报告中，我们呈现了两例三尖瓣口无瓣膜结构的病例，并对相关文献进行了综述。三尖瓣瓣膜结构完全缺失是一种非常罕见的异常情况，与肺动脉闭锁及完整室间隔并存，被称为三尖瓣口无瓣膜结构。双三尖瓣口及孤立性右位心是我们首例病例的显著特征。本报告的第二例患者为一名5岁男孩，是文献中首例将这种三尖瓣畸形作为孤立异常情况的病例，也是文献中首例存活病例。
