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多中心Castleman病中的自身免疫性溶血性贫血

Autoimmune hemolytic anemia in multicentric Castleman's disease.

作者信息

Liberato N L, Bollati P, Chiofalo F, Filipponi M, Poli M

机构信息

Divisione di Medicina, Ospedale C. Mira, Casorate Primo, Italy.

出版信息

Haematologica. 1996 Jan-Feb;81(1):40-43.

PMID:8900850
Abstract

We report on a patient affected by multicentric Castleman's disease who developed an acute immunohemolytic anemia due to warm antibody. The clinical course was characterized by refractoriness to the steroidal treatment and by a dramatic improvement of the hematological and objective picture following combination chemotherapy (CHOP regimen). The possible existence of a link between the lymphoproliferative syndrome and the immunological derangement is also discussed.

摘要

我们报告了一例患有多中心Castleman病的患者,该患者因温抗体导致急性免疫性溶血性贫血。临床病程的特点是对类固醇治疗无效,而联合化疗(CHOP方案)后血液学和客观症状显著改善。我们还讨论了淋巴增殖综合征与免疫紊乱之间可能存在的联系。

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引用本文的文献

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Idiopathic Multicentric Castleman Disease with Autoimmune Hemolytic Anemia and Production of Anti-drug Antibody against Tocilizumab.伴有自身免疫性溶血性贫血及抗托珠单抗药物抗体产生的特发性多中心Castleman病
Intern Med. 2019 Nov 15;58(22):3313-3318. doi: 10.2169/internalmedicine.2989-19. Epub 2019 Jul 10.
2
Treatment of Castleman's disease.卡斯尔曼病的治疗。
Curr Treat Options Oncol. 2005 May;6(3):255-66. doi: 10.1007/s11864-005-0008-z.