神经纤维瘤病的骨扫描：神经纤维瘤、丛状神经瘤和神经纤维肉瘤。
Bone scans in neurofibromatosis: neurofibroma, plexiform neuroma and neurofibrosarcoma.
作者信息
Kloos R T, Rufini V, Gross M D, Shapiro B
机构信息
Department of Internal Medicine, University of Michigan, Ann Arbor, USA.
出版信息
J Nucl Med. 1996 Nov;37(11):1778-83.
UNLABELLED
Neurofibromatosis type 1 or von Recklinghausen's disease is one of the most common autosomal dominant genetic disorders. Between 29% and 77% of patients may suffer from a wide range of skeletal abnormalities and, thus, patients with neurofibromatosis frequently undergo skeletal scintigraphy, at which time the common peripheral nerve soft-tissue tumors that occur in this syndrome (neurofibromas, plexiform neuromas and neurofibrosarcomas) may be demonstrated.
METHODS
Single or multiphase 99mTc methylenediphosphonate (MDP) bone scans were performed in five patients with neurofibromatosis as part of their clinical evaluation.
RESULTS
We imaged neurofibrosarcomas in three patients, cutaneous neurofibromas in one patient and a plexiform neuroma in one patient.
CONCLUSION
Single- or multiphasic bone scans may localize common soft-tissue tumors in neurofibromatosis.
未标注
1型神经纤维瘤病或冯·雷克林豪森病是最常见的常染色体显性遗传病之一。29%至77%的患者可能患有多种骨骼异常，因此，神经纤维瘤病患者经常接受骨骼闪烁扫描，此时可能会显示出该综合征中常见的周围神经软组织肿瘤（神经纤维瘤、丛状神经瘤和神经纤维肉瘤）。
方法
对5例神经纤维瘤病患者进行了单期或多期99m锝亚甲基二膦酸盐（MDP）骨扫描，作为其临床评估的一部分。
结果
我们在3例患者中成像了神经纤维肉瘤，1例患者成像了皮肤神经纤维瘤，1例患者成像了丛状神经瘤。
结论
单期或多期骨扫描可定位神经纤维瘤病中的常见软组织肿瘤。
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