Maresi E, Becchina G, Orlando E, Ottoveggio G
Istituto di Anatomia Patologica, Universit di Palermo.
Pathologica. 1995 Dec;87(6):666-71.
In this report the authors describe a rare case of pulmonary/renal syndrome like-Goodpasture's disease characterized by a necrotizing acute capillaritis in the lung, kidney, liver, spleen and heart. In the heart the capillaritis was associated with a contiguous acute ischemic lesion. The clinical and pathologic findings of the case suggest that the presence of vasculitis should not exclude a diagnosis of Goodpasture's Syndrome and that the multisystemic capillaritis would demonstrate the organ-non-specificity of anti-glomerular/alveolar basement membrane antibody.
在本报告中,作者描述了一例罕见的类似肺出血肾炎综合征(Goodpasture病)的肺/肾综合征病例,其特征为肺、肾、肝、脾和心脏出现坏死性急性毛细血管炎。在心脏中,毛细血管炎与相邻的急性缺血性病变相关。该病例的临床和病理表现提示,血管炎的存在不应排除肺出血肾炎综合征的诊断,且多系统毛细血管炎将显示抗肾小球/肺泡基底膜抗体的器官非特异性。