Chen M C, Hung J S, Chang K C, Lo P H, Chen Y C, Fu M
Section of Cardiology, Chang Gung Memorial Hospital, Taiwan, Republic of China.
J Ultrasound Med. 1996 Dec;15(12):875-9. doi: 10.7863/jum.1996.15.12.875.
Unroofed coronary sinus, a rare congenital anomaly first described by Raghib and colleagues1 in 1965, is a result of an embryologic error involving imperfect or complete failure of development of the left atriovenous fold, which is manifested as a focal (fenestration or partial unroofing of the coronary sinus) or complete absence of the coronary sinus septum. Before the era of echocardiography, precise diagnosis of this anomaly was possible only during surgical procedure or at autopsy. Since the advent of the echocardiography, several studies have reported the usefulness of two-dimensional transthoracic and transesophageal echocardiography in the diagnosis of unroofed coronary sinus. We describe the intracardiac echocardiographic delineation of partially unroofed coronary sinus and persistent left superior vena cava in a patient with atrioventricular nodal reentrant tachycardia. Incidental finding of the dilated coronary sinus during radio frequency ablation of the tachycardia led to the diagnosis of this unusual anomaly.
无顶冠状静脉窦是一种罕见的先天性异常，于1965年由拉吉卜及其同事首次描述，它是胚胎发育错误的结果，涉及左房室襞发育不完全或完全失败，表现为局灶性（冠状静脉窦开窗或部分无顶）或冠状静脉窦间隔完全缺失。在超声心动图时代之前，只有在手术过程中或尸检时才能对这种异常进行精确诊断。自超声心动图问世以来，多项研究报告了二维经胸和经食管超声心动图在诊断无顶冠状静脉窦中的作用。我们描述了一名患有房室结折返性心动过速患者的部分无顶冠状静脉窦和持续左上腔静脉的心内超声心动图描绘。在对心动过速进行射频消融期间偶然发现扩张的冠状静脉窦，从而诊断出这种不寻常的异常。
