Tanino T, Ohba N, Mishima S
Klin Monbl Augenheilkd. 1977 Jun;170(6):808-13.
Kinetic perimetry was carried out using the Goldmann perimeter in 201 patients with primary pigmentary retinal dystrophy, 156 autosomal recessive and 45 autosomal dominant cases. "The advanced stage" of the isopter deterioration was defined as the isopter area with the test object I-4 being 1 cm2 or less on the chart of Goldmann. The frequency of "the advanced stage" cases in creased with age in both hereditary forms, but it was higher in the recessive than in the dominant form throughout all age groups. The frequency-age relationship was exponential as is found in various aging phenomena. Fifty per cent of the patients were in "the advanced stage" at the age of 30 years in the recessive and at the age of 56 years in the dominent form.
使用戈德曼视野计对201例原发性色素性视网膜营养不良患者进行了动态视野检查,其中156例为常染色体隐性遗传病例,45例为常染色体显性遗传病例。等视线恶化的“晚期”定义为在戈德曼视野计图表上,测试目标I-4的等视线面积为1平方厘米或更小。在两种遗传形式中,“晚期”病例的发生率均随年龄增长而增加,但在所有年龄组中,隐性遗传形式的发生率均高于显性遗传形式。频率与年龄的关系呈指数关系,这在各种衰老现象中都有发现。隐性遗传形式的患者在30岁时,50%处于“晚期”;显性遗传形式的患者在56岁时,50%处于“晚期”。