Fleming M V, Travis W D
Department of Pulmonary and Mediastinal Pathology, Armed Forces Institute of Pathology, Washington, DC 20306-6000, USA.
Pathology (Phila). 1996;4(1):1-21.
Because the list of interstitial lung diseases is so extensive, encompassing more than 180 chronic lung diseases in which the interstitium is altered by inflammation and/or fibrosis, this chapter focuses on several inflammatory lung diseases of unknown etiology: usual interstitial pneumonitis, respiratory bronchiolitis, idiopathic bronchiolitis obliterans with organizing pneumonia, pulmonary Langerhans' cell granulomatosis, hypersensitivity pneumonitis, and lymphangioleiomyomatosis.
由于间质性肺疾病的种类繁多,涵盖了180多种慢性肺部疾病,其中间质因炎症和/或纤维化而发生改变,因此本章重点关注几种病因不明的炎症性肺部疾病:寻常型间质性肺炎、呼吸性细支气管炎、特发性闭塞性细支气管炎伴机化性肺炎、肺朗格汉斯细胞组织细胞增多症、过敏性肺炎和淋巴管平滑肌瘤病。