Ali S Z, Teichberg S, Kahn E, Hajdu S I
Department of Laboratories, North Shore University Hospital-Cornell University Medical College, Manhasset, New York 11030, USA.
Pediatr Pathol Lab Med. 1996 Jan-Feb;16(1):99-105.
Primary intrathoracic liposarcoma is an extremely rare neoplasm in the pediatric age group. We report an unusual case of a 3-year-old boy who presented with a large intrathoracic tumor arising from the right chest wall. Biopsy showed a pleomorphic sarcoma with histological, immunohistochemical, and ultrastructural features of pleomorphic liposarcoma. The tumor displayed an aggressive clinical behavior, and the patient continued to have recurrences despite rigorous chemotherapy and radiation treatment. He subsequently died 2 years after the initial diagnosis.
原发性胸内脂肪肉瘤在儿童年龄组中是一种极其罕见的肿瘤。我们报告了一例不寻常的病例，一名3岁男孩，其右胸壁出现一个巨大的胸内肿瘤。活检显示为多形性肉瘤，具有多形性脂肪肉瘤的组织学、免疫组化和超微结构特征。该肿瘤表现出侵袭性的临床行为，尽管进行了严格的化疗和放疗，患者仍持续复发。他在初次诊断后2年去世。
