Lang E K
Rev Interam Radiol. 1977 Jul;2(3):177-80.
Anorectal atresia with recto-urethral fistula is one of the most common congenital anomalies afflicting the hindgut (1,2). The "H-type" ano-urethral fistula, however, is relatively rare, similar to the "H-type" tracheo-esophageal fistula which is the least common such anomaly of that region. The association of an "H-type" tracheo-esophageal fistula and an "H-type" ano-urethral fistula and stricture of the anterior urethra is considered a rare combination of anomalies. Two cases of "H-type" ano-urethral fistula with stricture of the anterior urethra and associated in one instance with an "H-type" tracheo-esophageal fistula and the other with esophageal atresia and tracho-escophageal fistula are reported and comment is made on the interesting underlying embryologic defect.
直肠尿道瘘型肛门直肠闭锁是最常见的累及后肠的先天性畸形之一(1,2)。然而,“H型”肛门尿道瘘相对罕见,类似于“区域中最不常见的“H型”气管食管瘘。“H型”气管食管瘘与“H型”肛门尿道瘘以及前尿道狭窄被认为是一种罕见的畸形组合。本文报告了两例伴有前尿道狭窄的“H型”肛门尿道瘘病例,其中一例伴有“H型”气管食管瘘,另一例伴有食管闭锁和气管食管瘘,并对有趣的潜在胚胎学缺陷进行了讨论。