Abou-Elhmd K A, Hawthorne M R, Flood L M
Department of Otolaryngology, North Riding Infirmary, Middlesbrough, UK.
J Laryngol Otol. 1996 Oct;110(10):958-61. doi: 10.1017/s0022215100135455.
Cochlear implantation is now a routine clinical procedure for deaf patients in many countries (Gibson, 1987). It replaces the function of damaged cochlear hair cells and therefore, detects sound and by electrical stimulation produces an appropriate signal in the remaining cochlear nerve fibres (House and Berliner, 1991). Wegener's granulomatosis is an uncommon auto-immune disease. It has a peak incidence at the fifth decade with slight male predominance. Nasal problems are the predominant presentation with otological manifestations presenting rarely. We report a case of Wegener's granulomatosis presenting with total hearing loss and after right cochlear implantation a free field threshold of 40 dB and 20 per cent Bamford-Kowal-Bench (BKB) speech test. We conclude that Wegener's granulomatosis is not an absolute contraindication for cochlear implantation.
在许多国家，人工耳蜗植入术现已成为针对耳聋患者的常规临床手术（吉布森，1987年）。它替代受损的耳蜗毛细胞的功能，因此能检测声音，并通过电刺激在剩余的耳蜗神经纤维中产生适当的信号（豪斯和柏林纳，1991年）。韦格纳肉芽肿是一种罕见的自身免疫性疾病。其发病高峰在50岁左右，男性略占优势。鼻部问题是主要表现，耳部表现很少见。我们报告一例韦格纳肉芽肿患者，该患者全聋，在右侧人工耳蜗植入术后，自由声场阈值为40分贝，且在班福德-科瓦尔-本奇（BKB）言语测试中有20%的正确率。我们得出结论，韦格纳肉芽肿并非人工耳蜗植入的绝对禁忌证。
