Argo K M, Toriello H V, Jelsema R D, Zuidema L J
Division of Maternal-Fetal Medicine, West Michigan Perinatal and Genetic Diagnostic Center, Butterworth Hospital, Grand Rapids, Michigan, USA.
Ultrasound Obstet Gynecol. 1996 Nov;8(5):350-4. doi: 10.1046/j.1469-0705.1996.08050350.x.
Chondrodysplasia punctata, a skeletal dysplasia with craniofacial dysmorphism and joint contractures can occur with rhizomelia, mesomelia or both. The rhizomelic form is generally lethal, whereas one form of mesomelic chondrodysplasia punctata has been described that is associated with a presumably normal lifespan and intelligence. We describe a case of a fetus suspected prenatally of having rhizomelic chondrodysplasia punctata, who was subsequently diagnosed at 1.5 years of age to have the tibia-metacarpal form of chondrodysplasia punctata. The prenatal sonographic findings of second-trimester micromelic bone shortening and third-trimester proximal femoral stippling may be present in the rhizomelic form but are not specific to this condition.
点状软骨发育不良是一种伴有颅面畸形和关节挛缩的骨骼发育异常,可伴有近段肢体短小、中段肢体短小或两者皆有。近段肢体短小型通常是致死性的,而有一种中段肢体短小型点状软骨发育不良已被描述,其与大概正常的寿命和智力相关。我们描述了一例产前疑似患有近段肢体短小型点状软骨发育不良的胎儿,该胎儿随后在1.5岁时被诊断为胫-掌骨型点状软骨发育不良。孕中期肢体短小的超声检查结果以及孕晚期股骨近端斑点状表现可能见于近段肢体短小型,但并非该病症所特有。