Flynn J M, Otsuka N Y, Emans J B, Hall J E, Hresko M T
Children's Hospital, Boston, Massachusetts 02115, USA.
J Pediatr Orthop. 1997 Jan-Feb;17(1):100-4.
Segmental spinal dysgenesis is a rare congenital condition of the lumbar or thoracolumbar spine that can be associated with significant progressive or permanent neurologic defects, including paraplegia. In the past, both bracing and surgery have been recommended. Of the seven children we have seen with this problem, three have lost motor function between presentation and the time of surgery. Our experience suggests that to prevent catastrophic neurologic deterioration, surgery is indicated once the diagnosis is made.
节段性脊柱发育不全是一种罕见的腰椎或胸腰椎先天性疾病，可伴有严重的进行性或永久性神经缺陷，包括截瘫。过去，曾推荐过支具治疗和手术治疗。在我们所见到的患有此问题的7名儿童中，有3名在就诊至手术期间失去了运动功能。我们的经验表明，为防止灾难性的神经功能恶化，一旦确诊即应进行手术。
