Crepaz R, Knoll P, Pitscheider W
Divisione di Cardiologia, Ospedale Generale Regionale, Bolzano.
G Ital Cardiol. 1996 Oct;26(10):1195-201.
Corrected transposition of the great arteries (cTGA) is a rare condition, and few patients with this abnormality survive the 50th year of age because of associated anomalies or the subsequent development of left atrioventricular valve regurgitation or heart block or both. We report the case of a 75 years old man with cTGA without associated anomalies which seems to be of particular interest because of the following reasons: 1) cTGA is a rare condition in advanced age; 2) the diagnosis has been made by MRI which allowed a complete segmental analysis; 3) this case confirms that the morphologic right ventricle in systemic position can function appropriately over a long term. We conclude that MRI can be an alternative to Echocardiography in patients with complex congenital cardiac disease who exhibit a poor ultrasound window.
矫正型大动脉转位（cTGA）是一种罕见疾病，由于合并畸形或随后出现左房室瓣反流或心脏传导阻滞或两者兼有，很少有患有这种异常的患者能活到50岁。我们报告一例75岁男性患有cTGA且无合并畸形的病例，该病例似乎特别值得关注，原因如下：1）cTGA在高龄患者中罕见；2）通过磁共振成像（MRI）进行诊断，其允许进行完整的节段分析；3）该病例证实处于体循环位置的形态学右心室可长期正常发挥功能。我们得出结论，对于超声窗不佳的复杂先天性心脏病患者，MRI可作为超声心动图的替代检查方法。
