Sarriá A, Lázaro A, Lázaro J, Garagorri J, Sanz J, Bueno M
An Esp Pediatr. 1977 May;10(5):489-96.
A boy of 5 8/12 years of age affected with Shwachman's Syndrome is presented. He showed frequent respiratory infections that can be in order with a low account in T-lymphocytes found on immunological study. A cytoplasmic degenerative process was found after microscopical and ultrastructural vision of osteoid tissue, which is compatible with biochemical alterations.