Kobayashi S, Ohmori K, Sekiguchi J
Department of Plastic and Reconstructive Surgery, Tokyo Metropolitan Police Hospital, Japan.
J Craniofac Surg. 1995 Sep;6(5):382-5. doi: 10.1097/00001665-199509000-00011.
The facial anomaly of Johanson-Blizzard syndrome and its correction are described. The facial anomaly was characterized by cleft-like bony defects located in the inferomedial portion of the orbit apart from the hypoplastic maxilla and the absence of nasal alae. Correction of the facial skeleton was performed using a free vascularized iliac bone graft and tripartite osteotomy to correct the shape of the orbit and elongate the severely hypoplastic maxilla. Those procedures were effective to a certain degree in correcting the facial anomaly of Johanson-Blizzard syndrome.
本文描述了约翰森-布利兹综合征的面部异常及其矫正方法。该面部异常的特征为位于眼眶内下部分的裂隙样骨质缺损，上颌骨发育不全，且无鼻翼。采用游离带血管髂骨移植和三联截骨术矫正面部骨骼，以矫正眼眶形状并延长严重发育不全的上颌骨。这些手术在一定程度上有效地矫正了约翰森-布利兹综合征的面部异常。
