Lemon M A, Weston W L, Huff J C
University of Colorado Health Sciences Center, Department of Dermatology, Denver, USA.
Br J Dermatol. 1997 Jan;136(1):115-7.
Paraneoplastic pemphigus (PNP) is a rare condition virtually always seen in adults. We report a 13-year-old boy who developed PNP associated with Castleman's tumour. His condition mimicked Stevens-Johnson syndrome and responded to tumour resection and immunosuppressive therapy.
副肿瘤性天疱疮(PNP)是一种罕见疾病,几乎仅见于成年人。我们报告一名13岁男孩,他患了与Castleman肿瘤相关的PNP。他的病情类似史蒂文斯 - 约翰逊综合征,对肿瘤切除和免疫抑制治疗有反应。