Suri R K, Jha N K, Sarwal V
Department of Cardiovascular and Thoracic Surgery, Postgraduate Institute of Medical Education and Research, Chandigarh, India.
J Heart Valve Dis. 1997 Jan;6(1):63-6.
A case of parachute mitral valve (PMV) associated with multiple muscular ventricular septal defects (VSDs) is reported in a 16-year-old girl who presented with dyspnea and a cardiac murmur. In addition, there were deformities of the right ear lobe and kyphoscoliosis of the thoracolumbar spine since birth. A preoperative diagnosis was made using two-dimensional and Doppler echocardiography, cardiac catheterization and angiocardiography. PMV was found to be stenotic and mildly regurgitant. At surgery, mitral valvuloplasty, preservation of the native valve apparatus and Dacron patch closure of multiple muscular VSDs was achieved. The latest available case reports in the literature pertaining to PMV and associated deformities have been reviewed.
本文报道了一名16岁女性患者,其患有降落伞样二尖瓣(PMV)并伴有多个肌部室间隔缺损(VSD),表现为呼吸困难和心脏杂音。此外,患者自出生以来右耳垂畸形,胸腰椎脊柱侧弯。术前通过二维和多普勒超声心动图、心导管检查和心血管造影进行诊断。发现PMV存在狭窄并伴有轻度反流。手术中成功进行了二尖瓣成形术,保留了天然瓣膜装置,并使用涤纶补片闭合了多个肌部VSD。本文还回顾了文献中有关PMV及相关畸形的最新病例报告。