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四血管脐带与多种先天性异常相关。

Four-vessel umbilical cord associated with multiple congenital anomalies.

作者信息

Painter D, Russell P

出版信息

Obstet Gynecol. 1977 Oct;50(4):505-7.

PMID:904818
Abstract

A case is described in which it was found at autopsy that the umbilical cord of a macerated stillborn infant had four patent vessels (two arteries and two veins) throughout its length. This was due to a rare persistence of the caudal portion of the right umbilical vein. The infant had multiple congenital anomalies including complete thoracic ectopia cordis, a symmetrical bifid liver, severe bilateral cleft lip and palate with absent soft palate and uvula , and cecum mobile. The autopsy findings are detailed and the relevant literature and embryology briefly discussed.

摘要

描述了一例病例,在尸检时发现一名浸软死产婴儿的脐带全程有四条开放血管(两条动脉和两条静脉)。这是由于右脐静脉尾部罕见的持续存在所致。该婴儿有多种先天性异常,包括完全性胸外心脏异位、对称的双叶肝脏、严重的双侧唇腭裂伴软腭和悬雍垂缺如以及游动盲肠。详细介绍了尸检结果,并简要讨论了相关文献和胚胎学。

相似文献

1
Four-vessel umbilical cord associated with multiple congenital anomalies.四血管脐带与多种先天性异常相关。
Obstet Gynecol. 1977 Oct;50(4):505-7.
2
Four-vessel umbilical cord associated with multiple congenital anomalies: a case report and literature review.四血管脐带合并多种先天性畸形:一例报告及文献复习
Fetal Pediatr Pathol. 2011;30(2):98-105. doi: 10.3109/15513815.2010.524687.
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Supernumerary umbilical vein in a hydropic neonate with hypertrophic cardiomyopathy.
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Supernumerary umbilical vein resulting in a four-vessel umbilical cord.额外脐静脉导致脐带出现四血管。
Am J Perinatol. 1998 May;15(5):299-301. doi: 10.1055/s-2007-993947.
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[Persistence of right umbilical vein--a rare vascular abnormality of the umbilical cord].[右侧脐静脉持续存在——一种罕见的脐带血管异常]
Zentralbl Gynakol. 1977;99(14):891-4.
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[Study on the histopathological abnormalities of the umbilical cord].[脐带组织病理学异常研究]
Nihon Sanka Fujinka Gakkai Zasshi. 1985 Mar;37(3):329-35.
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Umbilical vein variations: review of the literature and a case report of a persistent right umbilical vein.
Teratology. 1988 Feb;37(2):95-100. doi: 10.1002/tera.1420370202.
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[Malformations with reduced and with complete number of umbilical arteries. Autopsy findings in 955 stillborn, premature and full-term infants].
Schweiz Med Wochenschr. 1971 Jun 5;101(22):824-7.
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Neonate with a single umbilical vessel: a case report.单脐动脉新生儿:一例报告。
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Abnormal systemic venous connection possibly associated with a persistent right umbilical vein; a case report.异常体静脉连接可能与持续性右脐静脉相关;一例病例报告。
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The Occurrence of Supernumerary Umbilical Cord Vessels: A Review for Practicing Clinicians.额外脐血管的发生:给临床医生的综述
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Umbilical venous catheter misplacement due to unexpected supernumerary patent umbilical artery.因意外存在额外的脐动脉导致脐静脉导管误置
Matern Health Neonatol Perinatol. 2025 May 1;11(1):11. doi: 10.1186/s40748-025-00209-8.
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Current Perspectives of Prenatal Sonography of Umbilical Cord Morphology.脐带形态产前超声检查的当前视角
Int J Womens Health. 2021 Oct 18;13:939-971. doi: 10.2147/IJWH.S278747. eCollection 2021.
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A partial supernumerary umbilical vein: a case report.一条部分多余的脐静脉:病例报告
J Med Case Rep. 2019 May 18;13(1):149. doi: 10.1186/s13256-019-2094-8.
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Three umbilical arteries resulting in a four-vessel umbilical cord in a stillbirth.死产儿出现三条脐动脉,形成一条有四支血管的脐带。
Int J Clin Exp Med. 2015 Mar 15;8(3):4682-5. eCollection 2015.
6
A multivessel umbilical cord with a single umbilical artery.一条具有单脐动脉的多血管脐带。
J Clin Diagn Res. 2013 Jul;7(7):1453-4. doi: 10.7860/JCDR/2013/5220.3153. Epub 2013 Jul 1.
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Supernumerary umbilical vein demonstrated by radiography of a 27-week-gestation neonate.孕27周新生儿X线检查显示存在额外脐静脉。
Pediatr Radiol. 2006 Jun;36(6):570. doi: 10.1007/s00247-005-0106-x. Epub 2006 Feb 28.