Rodríguez Rodríguez E, Santolaria Fernández F, González Reimers E, Alvarez Argüelles H, Cruz Díaz M, Rodríguez Moreno F, Oramas Rodríguez J
Servicio de Medicina Interna. Hospital Universitario de Canarias. La Laguna, Tenerife.
Rev Esp Enferm Dig. 1996 Dec;88(12):873-6.
We report the case of a woman with Caroli's syndrome (Caroli's disease and congenital hepatic fibrosis) and adult polycystic kidney disease. Whereas the association of these two entities with autosomal-recessive-polycystic kidney disease has been widely reported, its association with adult-polycystic kidney disease is very infrequent.