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[Caroli's disease, congenital hepatic fibrosis and renal polycystosis: a little frequent association].

作者信息

Rodríguez Rodríguez E, Santolaria Fernández F, González Reimers E, Alvarez Argüelles H, Cruz Díaz M, Rodríguez Moreno F, Oramas Rodríguez J

机构信息

Servicio de Medicina Interna. Hospital Universitario de Canarias. La Laguna, Tenerife.

出版信息

Rev Esp Enferm Dig. 1996 Dec;88(12):873-6.

PMID:9072058
Abstract

We report the case of a woman with Caroli's syndrome (Caroli's disease and congenital hepatic fibrosis) and adult polycystic kidney disease. Whereas the association of these two entities with autosomal-recessive-polycystic kidney disease has been widely reported, its association with adult-polycystic kidney disease is very infrequent.

摘要

相似文献

1
[Caroli's disease, congenital hepatic fibrosis and renal polycystosis: a little frequent association].
Rev Esp Enferm Dig. 1996 Dec;88(12):873-6.
2
Caroli's disease and congenital hepatic fibrosis associated with polycystic kidney disease. A case presenting with acute focal bacterial nephritis.卡罗里病及先天性肝纤维化合并多囊肾病。1例表现为急性局灶性细菌性肾炎的病例。
Clin Nephrol. 1992 Dec;38(6):324-8.
3
Caroli's disease and cystic kidney disease in a woman.一名女性的卡罗里病和多囊肾病
Nephron. 1996;73(2):310-1. doi: 10.1159/000189058.
4
[Clinical images in gastroenterology. Caroli's disease and congenital liver fibrosis].[胃肠病学临床影像。卡罗利病和先天性肝纤维化]
Rev Gastroenterol Mex. 1997 Jan-Mar;62(1):57.
5
[Association of congenital liver fibrosis, Caroli's disease and medullary renal cysts in 2 siblings].[2名同胞中先天性肝纤维化、卡罗里病和髓质肾囊肿的关联]
Radiol Med. 1994 Jul-Aug;88(1-2):162-4.
6
Polycystic kidney rat is a novel animal model of Caroli's disease associated with congenital hepatic fibrosis.多囊肾大鼠是一种与先天性肝纤维化相关的卡罗里病的新型动物模型。
Am J Pathol. 2001 May;158(5):1605-12. doi: 10.1016/S0002-9440(10)64116-8.
7
[Congenital hepatic fibrosis with Caroli's disease: report of three cases].先天性肝纤维化合并卡洛里病:三例报告
Zhonghua Gan Zang Bing Za Zhi. 2009 Aug;17(8):634-5.
8
[Caroli's disease and congenital liver fibrosis].[卡罗里病与先天性肝纤维化]
Duodecim. 1993;109(9):739-45.
9
A case of congenital intrahepatic biliary dilation (Caroli's disease).一例先天性肝内胆管扩张症(卡罗里病)。
Ceylon Med J. 1997 Mar;42(1):45.
10
[A case of Caroli's disease confirmed by pathology, atypical symptoms and images].[一例经病理、非典型症状及影像学检查确诊的卡罗里病病例]
Zhonghua Gan Zang Bing Za Zhi. 2021 Feb 20;29(2):172-174. doi: 10.3760/cma.j.cn501113-20191020-00384.

引用本文的文献

1
Incidentally detected polycystic kidney and Caroli's disease.偶然发现的多囊肾和卡罗里病。
Ann Gastroenterol. 2014;27(1):75.