Kothari M J, Bauer S B
Division of Neurology, Pennsylvania State University College of Medicine, Hershey 17033, USA.
J Child Neurol. 1997 Feb;12(2):97-100. doi: 10.1177/088307389701200205.
Diastematomyelia is a form of an occult dysraphism, which can present with lower urinary tract dysfunction. We present the findings in 21 patients with diastematomyelia evaluated at the Children's Hospital in Boston. Seventy-six percent of the patients were female. Eighty-six per cent had a cutaneous lesion present overlying the spine. Urodynamic and electrophysiologic studies showed abnormalities in 17 (81%) of 21 patients, of whom 13 (62%) had upper motor neuron dysfunction. Seventeen patients underwent corrective spinal surgery and none of the patients deteriorated on a follow-up urodynamic and electrophysiologic study. We recommend that patients with cutaneous, midline lower back lesions with or without lower urinary tract dysfunction be evaluated with a urodynamic and electrophysiologic study to characterize the extent of neurologic and urologic dysfunction.
脊髓纵裂是一种隐性脊柱裂，可表现为下尿路功能障碍。我们报告了在波士顿儿童医院评估的21例脊髓纵裂患者的研究结果。76%的患者为女性。86%的患者脊柱上方有皮肤病变。尿动力学和电生理研究显示，21例患者中有17例（81%）存在异常，其中13例（62%）有上运动神经元功能障碍。17例患者接受了脊柱矫正手术，在随访的尿动力学和电生理研究中，没有患者病情恶化。我们建议，对有或无下尿路功能障碍的下背部中线皮肤病变患者进行尿动力学和电生理研究，以确定神经和泌尿系统功能障碍的程度。
