Sang B C, Shi L, Dias P, Liu L, Wei J, Wang Z X, Monell C R, Behm F, Gruenwald S
Department of Molecular and Cell Biology, PharMingen Inc, San Diego, CA 92121, USA.
Blood. 1997 Apr 15;89(8):2909-14.
Nonrandom chromosomal abnormalities are found in most human malignancies, particularly leukemias and lymphomas. A characteristic t(1;19) (q23;p13.3) chromosomal translocation is detected in 5% of childhood acute lymphoblastic leukemia (ALL) cases. This translocation results in the formation of a fusion gene, which leads to the expression of an oncogenic E2A/pbx1 protein. Breakpoints in the E2A gene almost invariably occur within a single intron, and the identical portion of PBX1 is joined consistently to exon 13 of E2A in fusion mRNA. In this article, we report the development of monoclonal antibodies against E2A/pbx1 fusion protein using a specific peptide that corresponds to the junction region of the protein. The obtained antibodies recognize specifically the chimeric E2A/pbx1 fusion protein and lack cross-reactivities with E2A and pbx1. Immunohistochemical staining and flow cytometric studies show that these antibodies can distinguish t(1;19)-positive from t(1;19)-negative leukemic cells. These results indicate that the obtained E2A/pbx1-specific monoclonal antibodies might prove to be valuable diagnostic reagents and important tools for elucidating the mechanisms involved in oncogenesis and progression of t(1;19)-positive childhood ALL.
在大多数人类恶性肿瘤中都发现了非随机染色体异常,尤其是白血病和淋巴瘤。在5%的儿童急性淋巴细胞白血病(ALL)病例中检测到特征性的t(1;19) (q23;p13.3) 染色体易位。这种易位导致融合基因的形成,进而导致致癌性E2A/pbx1蛋白的表达。E2A基因的断点几乎总是发生在单个内含子内,并且PBX1的相同部分在融合mRNA中始终与E2A的外显子13相连。在本文中,我们报告了使用与该蛋白连接区域对应的特定肽段开发针对E2A/pbx1融合蛋白的单克隆抗体。所获得的抗体特异性识别嵌合的E2A/pbx1融合蛋白,并且与E2A和pbx1无交叉反应。免疫组织化学染色和流式细胞术研究表明,这些抗体可以区分t(1;19)阳性和t(1;19)阴性白血病细胞。这些结果表明,所获得的E2A/pbx1特异性单克隆抗体可能被证明是有价值的诊断试剂,也是阐明t(1;19)阳性儿童ALL发生和进展机制的重要工具。