De Cunto C L, Liberatore D I, San Román J L, Goldberg J C, Morandi A A, Feldman G
Pediatric Rheumatology Section, Hospital Italiano, Buenos Aires, Argentina.
J Pediatr. 1997 Apr;130(4):551-6. doi: 10.1016/s0022-3476(97)70238-5.
We describe four unrelated children with neonatal maculopapular rash, fever, arthritis, hepatosplenomegaly, lymphadenopathy, eye involvement, and neurologic symptoms. Radiographs of the joints were surprisingly similar, showing an abnormal epiphyseal and metaphyseal appearance. These clinical and radiologic findings allowed us to include these children in a very peculiar syndrome described as infantile-onset multisystemic inflammatory disease. A chondrosarcoma developed in one of our patients.
我们描述了4名无血缘关系的儿童,他们出现新生儿斑丘疹、发热、关节炎、肝脾肿大、淋巴结病、眼部受累及神经系统症状。关节的X线片惊人地相似,显示骨骺和干骺端外观异常。这些临床和影像学表现使我们将这些儿童纳入一种非常特殊的综合征,即婴儿期起病的多系统炎症性疾病。我们的一名患者发生了软骨肉瘤。