与色素失禁症相关的角膜异常。
Corneal abnormalities associated with incontinentia pigmenti.
作者信息
Ferreira R C, Ferreira L C, Forstot L, King R
机构信息
Department of Ophthalmology, Federal University of São Paulo.
出版信息
Am J Ophthalmol. 1997 Apr;123(4):549-51. doi: 10.1016/s0002-9394(14)70183-7.
PURPOSE
To report corneal abnormalities associated with incontinentia pigmenti.
CASE REPORTS
Two girls, aged 2 1/2 and 5 years, with incontinentia pigmenti from one family underwent a complete ophthalmic examination.
RESULTS
We found vortex (whorl-like) epithelial keratitis characterized by epithelial microcysts that stained with fluorescein and midstromal radial mild haziness in daughters of a family with incontinentia pigmenti.
CONCLUSION
Incontinentia pigmenti should be included in the differential diagnosis of children with keratitis, particularly if there is evidence of characteristic dermatologic or other systemic manifestations.
目的
报告与色素失禁症相关的角膜异常。
病例报告
来自同一家族的两名女童，年龄分别为2岁半和5岁，患有色素失禁症，接受了全面的眼科检查。
结果
我们在一个患有色素失禁症的家族的女儿中发现了涡状（螺旋状）上皮角膜炎，其特征为上皮微囊肿用荧光素染色，基质中部呈轻度放射状模糊。
结论
色素失禁症应纳入角膜炎患儿的鉴别诊断，特别是如果有特征性皮肤或其他全身表现的证据。
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