Moore T C
Division of Pediatric Surgery, Harbor-UCLA Medical Center, Torrance, CA, USA.
Semin Pediatr Surg. 1996 May;5(2):116-23.
Omphalomesenteric duct malformations comprise a wide spectrum of anatomic structures and associated symptoms (or no symptoms). They may range from a completely patent omphalomesenteric duct at the umbilicus to a variety of lesser remnants including cysts, fibrous cords connecting the umbilicus to the distal ileum, granulation tissue at the umbilicus, umbilical hernias, and the famous diverticulum of Meckel. Symptoms may involve fecal fistulas at the umbilicus, intussusception/prolapse of ileum at the umbilicus, intestinal obstruction from a variety of causes, melena and anemia, abdominal pain and inflammation, etc. Although symptoms occur most frequently during childhood years (especially in the first 2 years of life), they may occur through adult years as well. Although these malformations are found with equal frequency among the sexes, a significantly greater incidence of symptoms is encountered in males. Although one of the very most frequent malformations to be found (Meckel's diverticulum in 2% to 3% of the population), they are one of the most unlikely to cause symptoms (also Meckel's diverticulum). An awareness of the diversity of these malformations in type and symptomotology is essential to their proper and optimal management.
脐肠系膜管畸形包括多种解剖结构及相关症状(或无症状)。其范围可从脐部完全通畅的脐肠系膜管到各种较小的残余结构,包括囊肿、连接脐部与回肠远端的纤维索、脐部的肉芽组织、脐疝以及著名的梅克尔憩室。症状可能包括脐部粪瘘、脐部回肠套叠/脱垂、各种原因引起的肠梗阻、黑便和贫血、腹痛及炎症等。虽然症状最常出现在儿童期(尤其是生命的头两年),但也可能发生在成年期。尽管这些畸形在男女中的发现频率相同,但男性出现症状的发生率明显更高。虽然它们是最常发现的畸形之一(人群中2%至3%有梅克尔憩室),但也是最不太可能引起症状的畸形之一(同样是梅克尔憩室)。了解这些畸形在类型和症状学上的多样性对于其恰当和最佳管理至关重要。