Henderson W, Huckell V F, English J C, Fradet G
Vancouver Hospital, British Columbia.
Can J Cardiol. 1997 Apr;13(4):387-90.
Right outflow tract obstruction due to neurofibroma is rare, with only four cases identified in the world literature. Obstruction due to a pedunculated neurofibroma has never been reported. A 36-year-old woman with no known heart disease presenting with dyspnea, palpitations and chest pain was shown on echocardiogram to have a mobile right ventricular mass. Cardiac catheterization revealed normal coronary arteries and right ventricular outflow tract obstruction by a pedunculated mass, which was surgically removed and histologically proven to be a benign neurofibroma. Following surgery the patient's symptoms disappeared, with no recurrence three years postoperatively.
神经纤维瘤导致的右心室流出道梗阻较为罕见，世界文献中仅报道过4例。带蒂神经纤维瘤导致的梗阻从未有过报道。一名36岁无已知心脏病史的女性，因呼吸困难、心悸和胸痛就诊，超声心动图显示右心室有一活动肿物。心导管检查显示冠状动脉正常，右心室流出道被一带蒂肿物梗阻，该肿物经手术切除，组织学检查证实为良性神经纤维瘤。术后患者症状消失，术后三年无复发。
