Kim K A, Vincent W R, Muenchow S K, Wells W J, Downey S E
Division of Plastic and Reconstructive Surgery, Childrens Hospital Los Angeles, CA 90027, USA.
Ann Plast Surg. 1997 May;38(5):518-22. doi: 10.1097/00000637-199705000-00013.
Ectopia cordis is a very rare congenital anomaly associated with a high mortality rate. A successful repair of ectopia cordis with complete absence of sternum was achieved in a two-stage procedure. Initial management consisted of coverage of skin over the malpositioned heart using bilateral pectoral skin flaps. A second more definitive repair was undertaken at age 14 months. Four methyl methacrylate struts were used to reconstruct the anterior chest wall and were then covered with bilateral pectoralis major muscle flaps. At the 2.5-year follow-up there is no evidence of cardiopulmonary compromise and the development of the thorax appears normal. We advise that use of alloplastic materials is a valid option in managing this difficult congenital anomaly.
心脏异位是一种非常罕见的先天性异常，死亡率很高。通过两阶段手术成功修复了完全没有胸骨的心脏异位。初始治疗包括使用双侧胸壁皮瓣覆盖位置异常的心脏表面皮肤。在14个月大时进行了第二次更确定性的修复。使用四个甲基丙烯酸甲酯支柱重建前胸壁，然后用双侧胸大肌皮瓣覆盖。在2.5年的随访中，没有心肺功能受损的证据，胸部发育看起来正常。我们建议，在处理这种困难的先天性异常时，使用异体材料是一种有效的选择。
