Sakamoto T, Harada Y, Takeuchi T, Ohta K, Satomi G, Yasukochi S, Kano H, Tamura M, Yamazaki T, Ohta Y
Division of Cardiovascular Surgery, Nagano Children's Hospital, Japan.
Kyobu Geka. 1997 Jun;50(6):487-91.
We report a surgical case of severe Ebstein's anomaly associated with pulmonary atresia in the neonate. The baby had remarkable cardiomegaly (CTR > or = 90%) soon after birth and presented severe respiratory distress. He underwent modified Starnes operation (closure of tricuspid valve using a perforated patch, enlargement of interatrial communication, modified Blalock shunt, and PDA ligation) at the age of 12 days. He survived the procedure and cardiopulmonary failure was improved. However, he died from arrhythmia on the 3rd postoperative day. We think this procedure is useful regard to improvement of cardiopulmonary failure due to this fatal congenital heart disease.
我们报告一例新生儿严重埃布斯坦畸形合并肺动脉闭锁的外科病例。该婴儿出生后不久即出现显著的心扩大（心胸比率≥90%），并表现出严重的呼吸窘迫。他在12日龄时接受了改良的斯塔内斯手术（使用带孔补片关闭三尖瓣、扩大房间交通、改良布莱洛克分流术和动脉导管未闭结扎术）。他术后存活，心肺功能衰竭得到改善。然而，他在术后第3天死于心律失常。我们认为该手术对于改善这种致命性先天性心脏病所致的心肺功能衰竭是有用的。
