Kurien A, John P R, Milford D V
Department of Nephrology, Birmingham Children's Hospital, Ladywood Middleway.
Arch Dis Child. 1997 May;76(5):454-5. doi: 10.1136/adc.76.5.454.
A 4 year old girl with neurofibromatosis type 1 (NF1) was referred for hypertension. An aortogram showed narrowing of the left main renal artery. An angiogram three and a half years later showed coarctation of the abdominal aorta. She underwent aortoplasty but the stenosis recurred. Vascular involvement in NF1 may be progressive and requires long term follow up.
一名患有1型神经纤维瘤病(NF1)的4岁女孩因高血压前来就诊。主动脉造影显示左肾动脉主干狭窄。三年半后的血管造影显示腹主动脉缩窄。她接受了主动脉成形术,但狭窄复发。NF1中的血管受累可能是进行性的,需要长期随访。