Okada K, Eishi K, Takamoto S, Ando M, Kosakai Y, Nakano K, Sasako Y, Kobayashi J
Department of Cardiovascular Surgery, National Cardiovascular Center, Osaka, Japan.
Ann Thorac Surg. 1997 Jul;64(1):116-9. doi: 10.1016/s0003-4975(97)00365-2.
Behçet's aortitis is one of the most severe manifestations of Behçet's disease. However, there have been few reports of this rare entity. This article we describe our experience with surgical treatment of Behçet's aortitis in 8 patients.
From May 1978 to February 1995, we operated on 8 patients with Behçet's aortitis. All patients were followed up for a total of 54.4 patient-years (mean, 6.8 years).
There were no operative deaths, but 1 patient died in the hospital of ventricular fibrillation. Another death occurred as a result of pseudoaneurysm rupture 10 months after operation. Fourteen operations were performed on eight patients: a second operation was performed on four patients, and a third operation was performed on two patients. The translocated Bentall procedure, a modified Bentall procedure, was performed six times. One patient required a second operation for graft detachment, but the others have done well without further surgical intervention. Aortic valve replacement was performed six times, and three reoperations were needed after aortic valve replacement.
The translocated Bentall procedure may be effective for Behçet's aortitis, but further investigation is necessary.
白塞氏主动脉炎是白塞氏病最严重的表现之一。然而，关于这种罕见病症的报道很少。本文描述了我们对8例白塞氏主动脉炎患者进行手术治疗的经验。
1978年5月至1995年2月，我们对8例白塞氏主动脉炎患者进行了手术。所有患者共随访54.4患者年（平均6.8年）。
无手术死亡，但1例患者在医院死于心室颤动。另1例死亡发生在术后10个月，因假性动脉瘤破裂。8例患者共进行了14次手术：4例患者进行了第二次手术，2例患者进行了第三次手术。移位Bentall手术（一种改良的Bentall手术）进行了6次。1例患者因移植物脱离需要进行第二次手术，但其他患者未经进一步手术干预情况良好。进行了6次主动脉瓣置换，主动脉瓣置换后需要3次再次手术。
移位Bentall手术可能对白塞氏主动脉炎有效，但需要进一步研究。
