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Neonatal protein-losing enteropathy caused by intestinal lymphatic hypoplasia in siblings.

作者信息

Hardikar W, Smith A L, Chow C W

机构信息

Department of Gastroenterology, Royal Children's Hospital, Melbourne, Australia.

出版信息

J Pediatr Gastroenterol Nutr. 1997 Aug;25(2):217-21. doi: 10.1097/00005176-199708000-00016.

DOI:10.1097/00005176-199708000-00016
PMID:9252912
Abstract
摘要

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Neonatal protein-losing enteropathy caused by intestinal lymphatic hypoplasia in siblings.同胞中由肠道淋巴管发育不全引起的新生儿蛋白丢失性肠病。
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Congenital intestinal lymphatic hypoplasia presenting as non-immune hydrops in utero, and subsequent neonatal protein-losing enteropathy.先天性肠道淋巴管发育不全在子宫内表现为非免疫性水肿,随后在新生儿期出现蛋白丢失性肠病。
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[Congenital intestinal lymphangiectasia: a rare differential diagnosis in hypoproteinemia in infants].[先天性肠淋巴管扩张症:婴儿低蛋白血症的一种罕见鉴别诊断]
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Characteristic endoscopic features of intestinal lymphangiectasia: correlation with histological findings.肠道淋巴管扩张症的特征性内镜表现:与组织学结果的相关性
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A case of protein-losing enteropathy caused by intestinal lymphangiectasia in a preterm infant.一例早产儿因肠道淋巴管扩张症导致的蛋白丢失性肠病。
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Acquired intestinal lymphangiectasia successfully treated with a low-fat and medium-chain triacylglycerol-enriched diet in a patient with liver transplantation.肝移植患者采用低脂、富含中链甘油三酯饮食成功治疗获得性肠淋巴管扩张症。
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[Intestinal lymphangiectasia diagnosed by duodenoscopy and aimed biopsy].
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Clinicopathologic consideration of protein-losing enteropathy due to lymphangiectasia of the intestine.肠道淋巴管扩张症所致蛋白丢失性肠病的临床病理分析
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Pathophysiology, Diagnosis, and Management of Canine Intestinal Lymphangiectasia: A Comparative Review.犬肠道淋巴管扩张症的病理生理学、诊断与管理:一项比较性综述
Animals (Basel). 2022 Oct 15;12(20):2791. doi: 10.3390/ani12202791.
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Small Intestinal Lymphatic Hypoplasia in Three Dogs with Clinical Signs of Protein-losing Enteropathy.三只出现蛋白丢失性肠病临床症状的犬的小肠淋巴管发育不全
J Comp Pathol. 2018 Apr;160:39-49. doi: 10.1016/j.jcpa.2018.02.005. Epub 2018 Apr 4.
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Gastrointestinal lymphatics in health and disease.健康与疾病状态下的胃肠道淋巴管
Pathophysiology. 2010 Sep;17(4):315-35. doi: 10.1016/j.pathophys.2009.09.003.