[Creutzfeldt-Jakob disease].

A most common form of human prion disease, also known as non-conventional slow virus diseases; Creutzfeldt-Jakob's disease is described in detail. The available data on the pathogenesis of the illness have recently changed and constitute a most exciting article of contemporary medicine. 109 cases are introduced that have been verified neuropathologically in Hungary until now; their summed up clinical data, the pathological findings and their epidemiological characteristics are discussed. It must be emphasized that the diagnosis of the illness cannot be inevitably confirmed clinically. Transplantation of organs or tissues of all deceased, who suffered of an illness with dementia, should be strictly avoided accordingly.