Ribeiro R A, Romano A R, Birman E G, Mayer M P
School of Dentistry, Federal University of Juiz de Fora, Brazil.
Pediatr Dent. 1997 Jul-Aug;19(5):349-52.
Seventeen patients with a mean age of 7.33 (range 2.7-12.7) years with Rett syndrome (a progressive neurological disorder that occurs mainly in females) were evaluated for oral manifestations and habits. The most frequent habits were digit/hand sucking and/or biting (17/17), bruxism (14/17), mouth breathing (7/17), drooling (5/17), and tongue thrusting (5/17). Gingivitis (13/17) was the most common alteration of soft tissues. Only 2.7% of tooth surfaces were decayed. Nonphysiological dental attrition was present in 71% (12/17) of the children. Palatal shelving could be observed in 53% (9/17) of the children, probably related to the digit/hand sucking and/or biting habits. A high prevalence of anterior open bite (9/17) was observed. No patients exhibited anomalies of tooth number, size, form, structure, or eruption.
对17名平均年龄为7.33岁（范围2.7 - 12.7岁）的雷特综合征（一种主要发生在女性中的进行性神经疾病）患者进行了口腔表现和习惯的评估。最常见的习惯是手指/手部吸吮和/或啃咬（17/17）、磨牙症（14/17）、口呼吸（7/17）、流口水（5/17）和吐舌（5/17）。牙龈炎（13/17）是最常见的软组织改变。仅有2.7%的牙面有龋坏。71%（12/17）的儿童存在非生理性牙齿磨损。53%（9/17）的儿童可观察到腭架，这可能与手指/手部吸吮和/或啃咬习惯有关。观察到较高比例的前牙开（9/17）。没有患者表现出牙数、大小、形态、结构或萌出异常。
