Matteucci C, Busi G, Biferali F, Paventi S
Servizio di Cardiologia, Ospedale di Subiaco, Roma.
G Ital Cardiol. 1997 Jun;27(6):583-7.
Rhabdomyoma (RBD) is the commonest cardiac tumour in early childhood. This tumour, which is asymptomatic in most patients, is often associated with tuberous sclerosis, a multisystem disease that involves mainly the central nervous system. RBD, which is generally considered a hamartoma rather than true tumour, often regresses spontaneously by age of 2. We present the case of a 19 year-old male affected with an RBD diagnosed through transthoracic and transesophageal echocardiography and nuclear magnetic resonance imaging, and characterized by late cardiac manifestations, including intermittent left bundle branch block and a pseudo-ischemic electrocardiographic pattern. These findings may depend on the anterobasal septal localization of the RBD.