Kashyap R, Saxena R, Choudhry V P
Department of Haematology, All India Institute of Medical Sciences, New Delhi, India.
Haematologia (Budap). 1996;28(1):13-9.
Twenty four cases with rare coagulation disorders were diagnosed over a 4 year period. These included 8 patients with factor X deficiency, 7 with factor XIII deficiency, 4 each with fibrinogen and factor VII deficiency and 1 with factor V deficiency. All these patients had presented with bleeding manifestations. Two patients with factor X deficiency showed interesting clinical presentations, one patient had recurrent deep vein thrombosis and another patient had a pseudotumor of the thigh.
在4年期间共诊断出24例罕见凝血障碍病例。其中包括8例X因子缺乏患者、7例XIII因子缺乏患者、4例纤维蛋白原缺乏患者和4例VII因子缺乏患者，以及1例V因子缺乏患者。所有这些患者均有出血表现。2例X因子缺乏患者有有趣的临床表现，1例患者反复发生深静脉血栓形成，另1例患者有大腿假肿瘤。
