Shahlaee A H, Burton E M, Sabio H, Plouffe L, Teeslink R
Department of Pediatrics, Medical College of Georgia, Augusta, Georgia, USA.
Pediatr Radiol. 1997 Sep;27(9):755-7. doi: 10.1007/s002470050219.
Chylous reflux is a manifestation of primary or secondary lymphatic obstruction. Primary lymphatic obstruction is defined as lymphangiectasia and incompetency of lymphatic valves without an underlying cause. Lymphangiectasia resulting from trauma, neoplasm, irradiation, or inflammation characterizes secondary lymphatic obstruction. Leakage of chyle into the uterus, vagina, bladder, or rectum can occur with either primary or secondary lymphatic obstruction. We report a patient with chylous vaginal discharge, a rare presentation of primary chylous reflux syndrome. CT-lymphangiography and magnetic resonance imaging clearly depicted this disorder. To our knowledge, only 20 cases of chylous vaginal discharge have been reported previously; chylous vaginal drainage occurred in the absence of chylous uterine reflux in only three. Although this is a rare anomaly, chylous reflux should be considered in a child with chronic vaginal discharge and lower extremity swelling.
乳糜反流是原发性或继发性淋巴管阻塞的一种表现。原发性淋巴管阻塞定义为淋巴管扩张和淋巴管瓣膜功能不全且无潜在病因。由创伤、肿瘤、放射或炎症引起的淋巴管扩张是继发性淋巴管阻塞的特征。原发性或继发性淋巴管阻塞均可导致乳糜漏入子宫、阴道、膀胱或直肠。我们报告一例乳糜性阴道分泌物患者，这是原发性乳糜反流综合征的罕见表现。CT淋巴管造影和磁共振成像清晰地显示了这种疾病。据我们所知，此前仅报道过20例乳糜性阴道分泌物病例；仅3例乳糜性阴道引流发生时无乳糜性子宫反流。尽管这是一种罕见的异常情况，但对于患有慢性阴道分泌物和下肢肿胀的儿童应考虑乳糜反流。
