Vandenbroucke J, van Ooy A, Geukers C, van der Linden A J, Hoogmartens M
Department of Orthopaedic Surgery and Traumatology, Academisch Ziekenhuis Maastricht, The Netherlands.
Eur Spine J. 1997;6(4):273-7. doi: 10.1007/BF01322451.
We report two cases of dystrophic scoliosis in neurofibromatosis, each of particular interest. In the first, kyphosis was present with vertebral rotatory subluxation but no neurologic impairment, while the second patient showed manifest paraplegia due to rapidly progressive kyphoscoliosis. The importance of early surgical stabilisation, both front and back if possible, is stressed. Very sharp curves with progressive myelopathy should not be treated with halo-femoral traction because of the potential danger of evoking permanent paraplegia.
我们报告了两例神经纤维瘤病性营养不良性脊柱侧凸病例,每例都有特别之处。第一例,存在脊柱后凸伴椎体旋转半脱位,但无神经功能损害;而第二例患者因快速进展的脊柱后凸侧凸出现明显截瘫。强调了早期手术稳定的重要性,如有可能应进行前路和后路手术。对于伴有进行性脊髓病的非常尖锐的曲线,不应采用头-股牵引治疗,因为有引发永久性截瘫的潜在危险。