Marui A, Mochizuki T, Mitsui N, Koyama T, Horibe M
Department of Cardiovascular Surgery, Akane-Foundation Tsuchiya General Hospital, Hiroshima, Japan.
Nihon Kyobu Geka Gakkai Zasshi. 1997 Aug;45(8):1189-94.
Three patients with anomalous origin of the right pulmonary artery from the ascending aorta were reported. Case 1: A 33-day-old premature infant (body weight 984 g) with the right pulmonary artery arising from the ascending aorta (RAPAA) and the patent ductus arteriosus (PDA). Banding of the right pulmonary artery (RPAB) and ligation of PDA were performed as a palliative operation. AT 3-month-old (BW 2,200 g), division and direct anastomosis of the anomalous vessel to the main pulmonary trunk was done as a radical operation under hypothermic cardiopulmonary bypass (CPB). Case 2: A 16-day-old infant with RAPAA and PDA. Division and direct anastomosis of the anomalous vessel to the main pulmonary trunk and ligation of PDA were performed as a radical operation under hypothermic CPB. Case 3: A 74-day-old infant with RAPAA and Ebstein's anomaly. RPAB was performed as a first palliative operation and left Blalock-Taussig shunt as a second operation. Glenn operation is scheduled as third operation prior to Fontan type operation.
报道了3例右肺动脉起源于升主动脉的病例。病例1：一名33天的早产儿（体重984克），右肺动脉起源于升主动脉（RAPAA）且动脉导管未闭（PDA）。作为姑息性手术，进行了右肺动脉环扎术（RPAB）和PDA结扎术。3个月大（体重2200克）时，在低温体外循环（CPB）下进行了异常血管与主肺动脉干的离断及直接吻合术，作为根治性手术。病例2：一名16天的婴儿，患有RAPAA和PDA。在低温CPB下进行了异常血管与主肺动脉干的离断及直接吻合术和PDA结扎术，作为根治性手术。病例3：一名74天的婴儿，患有RAPAA和埃布斯坦畸形。作为首次姑息性手术进行了RPAB，第二次手术进行了左布莱洛克 - 陶西格分流术。计划在Fontan类手术之前进行第三次手术，即格林手术。
