Ortigado Matamala A, Martínez Granero M A, Pascual Castroviejo I
Servicio de Neurología Infantil, Hospital Infantil La Paz, Madrid.
Neurologia. 1997 Jun-Jul;12(6):256-8.
Scleroderma en coup de sabre is a descriptive term denoting linear scleroderma of the frontoparietal area of the face and scalp. This form of scleroderma is infrequent, mainly in pediatric patients, but not infrequently associates neurologic symptoms, especially epilepsy. We describe a 15-year-old girl with scleroderma en coup de sabre and a long-standing history of epilepsy. Cranial magnetic resonance examination reaffirms the clinical impression that inflammation is not solely confined to the skin in this form of linear scleroderma.
剑伤性硬皮病是一个描述性术语，指面部和头皮额顶区域的线状硬皮病。这种硬皮病形式并不常见，主要见于儿科患者，但常伴有神经症状，尤其是癫痫。我们描述了一名患有剑伤性硬皮病且有长期癫痫病史的15岁女孩。头颅磁共振检查再次证实了临床印象，即在这种线状硬皮病形式中，炎症不仅局限于皮肤。
