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心电图在确定强直性肌营养不良患者心脏事件及死亡率方面的价值

Value of the electrocardiogram in determining cardiac events and mortality in myotonic dystrophy.

作者信息

Colleran J A, Hawley R J, Pinnow E E, Kokkinos P F, Fletcher R D

机构信息

Department of Neurology, Georgetown University Medical Center, Washington, D.C., USA.

出版信息

Am J Cardiol. 1997 Dec 1;80(11):1494-7. doi: 10.1016/s0002-9149(97)00742-x.

Abstract

Electrocardiograms were recorded at baseline and regular intervals in 53 patients with myotonic dystrophy who were followed for a mean of 6.3 +/- 4.0 years. Patients with cardiac events had a significantly prolonged PR interval (p <0.001), a later age of onset of neuromuscular symptoms (p <0.05), and were older (p <0.005).

摘要

对53例强直性肌营养不良患者在基线时及定期进行心电图记录,随访时间平均为6.3±4.0年。发生心脏事件的患者PR间期显著延长(p<0.001),神经肌肉症状发病年龄较晚(p<0.05),且年龄较大(p<0.005)。

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