Pediatrics. 1976 May;57(5):783-92.
A sufficient variety of semisynthetic dietary products is now available to permit control of amino acid imbalance in several inborn errors of metabolism. However, they must be used carefully, and their effects monitored closely. Continuing development of products for this type of special diet--to provide a wider variety--is necessary. Regionalization of treatment programs for patients with inborn errors of metabolism is recommended. Metabolic centers which are accumulating experience and have good laboratory support may be the most efficient way of providing adequate treatment for patients with inborn errors of metabolism.
现在有足够种类的半合成膳食产品可用于控制几种先天性代谢缺陷中的氨基酸失衡。然而,必须谨慎使用这些产品,并密切监测其效果。继续开发此类特殊饮食的产品以提供更多种类是必要的。建议对先天性代谢缺陷患者的治疗方案进行区域化。积累了经验并拥有良好实验室支持的代谢中心可能是为先天性代谢缺陷患者提供充分治疗的最有效方式。