Honey M, Pearson M C, Pattinson J N
Thorax. 1976 Apr;31(2):190-6. doi: 10.1136/thx.31.2.190.
A man aged 29 was first seen at the age of 11, when he was found to have a congenital anomaly of the pulmonary veins which follow an abnormal course to the hilum. On the left side, two large veins descend peripherally before turning medially towards the left atrium; on the right, several smaller veins follow a similar circuitous route from the periphery, before uniting into two main veins which enter the left atrium. The proximal pulmonary arteries are normal in their pattern of branching and distribution but are dilated and tortous and taper abruptly: the left lower lobe artery is abnormally large almost down to the diaphragm. There is also a systemic arterio/pulmonary venous fistula. There is no haemodynamic disturbance, but gas transfer is slightly impaired, and there is slight arterial desaturation. The congenital anomaly is unique. Reported cases described as having pulmonary venous varices are a heterogeneous group, but one patient described as such shows resemblances to our case.
一名29岁男性在11岁时首次就诊，当时发现他存在肺静脉先天性异常，肺静脉走行异常至肺门。在左侧，两条大静脉先向周边下行，然后转向内侧朝向左心房；在右侧，几条较小的静脉从周边走类似的迂回路线，然后合并成两条主要静脉进入左心房。近端肺动脉的分支和分布模式正常，但扩张且迂曲，突然变细：左下叶动脉异常粗大，几乎直至膈肌水平。还存在体动脉/肺静脉瘘。无血流动力学紊乱，但气体交换略有受损，且有轻度动脉血氧饱和度降低。这种先天性异常很独特。报道中被描述为患有肺静脉静脉曲张的病例是一个异质性群体，但有一名被如此描述的患者与我们的病例有相似之处。
