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因胰胆管汇合异常所致的后天性胆总管囊肿。

Acquired choledochal cyst from anomalous pancreatobiliary duct union.

作者信息

Han S J, Hwang E H, Chung K S, Kim M J, Kim H

机构信息

Department of Pediatric Surgery, Yonsei University College of Medicine, Seoul, Korea.

出版信息

J Pediatr Surg. 1997 Dec;32(12):1735-8. doi: 10.1016/s0022-3468(97)90519-4.

DOI:10.1016/s0022-3468(97)90519-4
PMID:9434012
Abstract

The high incidence of anomalous pancreatobiliary duct union (APBDU) in children who have a choledochal cyst has been well documented. Additionally, cylindrical dilatation of the bile duct has been reproduced in animal models by anastomosing the pancreatic duct to the bile duct. In recent years, APBDU has been considered a possible etiologic factor in the formation of a choledochal cyst. The authors observed a progressive cylindrical dilatation of the common bile duct in a 6-year-old boy over an 18-month period. An operative cholangiogram showed a type Ic choledochal cyst and a type B APBDU (Todani classification). This clinical experience suggests that a normal common bile duct in children can be progressively dilated and become an acquired choledochal cyst arising as a complication of the preexisting APBDU.

摘要

胆总管囊肿患儿中胰胆管合流异常(APBDU)的高发病率已有充分记录。此外,通过将胰管与胆管吻合,已在动物模型中重现了胆管的圆柱形扩张。近年来,APBDU被认为是胆总管囊肿形成的一个可能病因。作者观察到一名6岁男孩在18个月内胆总管出现进行性圆柱形扩张。术中胆管造影显示为Ic型胆总管囊肿和B型APBDU(托达尼分类)。这一临床经验表明,儿童正常的胆总管可逐渐扩张,并成为作为先前存在的APBDU并发症而出现的后天性胆总管囊肿。

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