Morioka M, Furukawa Y, Kobayashi T, Tanaka H, Ohashi Y, Jin T X
Department of Urology, Kawasaki Medical School, Kurashiki, Japan.
Endocr J. 1997 Aug;44(4):547-52. doi: 10.1507/endocrj.44.547.
A case of hyperaldosteronism caused by adrenal cortical cancer observed in a 32-year-old man was reported. The patient showed marked hypertension and hypokalemia, but neither obesity nor hyperglycemia was observed. Endocrine studies revealed hyperaldosteronism and concurrent excessive secretion of cortisol, but diurnal rhythms of plasma ACTH and cortisol were normal. Imaging studies revealed a large left adrenal mass, and the positive accumulation of radiolabelled material by adrenal scintigraphy was observed both in the tumor and the contralateral adrenal gland. The removed tumor was predominantly composed of dark compact cells with marked nuclear pleomorphism, and mitotic figures and sinusoidal invasion were also observed. The analysis of steroidogenic enzyme activities revealed that the activity of aldosterone-synthesizing enzyme (P-450aldo) which was usually undetectable in normal adrenal tissues and adenomas other than aldosterone-producing adenoma (APA) was detectable as one-third of that of APA. Although activities of other enzymes were reduced, the expression of P-450aldo activity was considered to be the specific character of this cancer.
报告了一名32岁男性患者,其患有由肾上腺皮质癌引起的醛固酮增多症。该患者表现出明显的高血压和低钾血症,但未观察到肥胖或高血糖。内分泌研究显示醛固酮增多症,同时伴有皮质醇分泌过多,但血浆促肾上腺皮质激素(ACTH)和皮质醇的昼夜节律正常。影像学研究显示左肾上腺有一个大肿块,肾上腺闪烁显像显示肿瘤及对侧肾上腺均有放射性标记物质的阳性聚集。切除的肿瘤主要由深色致密细胞组成,具有明显的核多形性,还观察到有丝分裂象和窦状隙浸润。对类固醇生成酶活性的分析表明,醛固酮合成酶(P-450aldo)的活性在正常肾上腺组织和除醛固酮瘤(APA)以外的腺瘤中通常检测不到,而在此肿瘤中可检测到,其活性为APA的三分之一。尽管其他酶的活性降低,但P-450aldo活性的表达被认为是这种癌症的特异性特征。