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新生儿埃布斯坦畸形的三尖瓣关闭

Tricuspid valve closure for neonatal Ebstein's anomaly.

作者信息

Endo M, Ohmi M, Sato K, Tanaka T, Kakizawa H, Tabayashi K

机构信息

Department of Thoracic and Cardiovascular Surgery, Tohoku University School of Medicine, Sendai, Japan.

出版信息

Ann Thorac Surg. 1998 Feb;65(2):540-2. doi: 10.1016/s0003-4975(97)01357-x.

Abstract

A respirator-dependent 11-day-old boy with Ebstein's anomaly is presented. His cardiac anomaly with progressive cardiomegaly was first noticed at 24 weeks' gestation on fetal echocardiography. After birth, he required mechanical ventilation because of massive tricuspid regurgitation and restricted pulmonary blood flow. The operation of tricuspid valve patch closure, resection of right atrial wall, and central shunt successfully weaned him from the respirator on postoperative day 13. Cavopulmonary anastomosis was performed without problem when the patient was 8 months of age.

摘要

本文介绍了一名患有埃布斯坦畸形的11日龄依赖呼吸机的男婴。他的心脏畸形伴有进行性心脏扩大,在孕24周时通过胎儿超声心动图首次被发现。出生后,由于大量三尖瓣反流和肺血流受限,他需要机械通气。三尖瓣补片闭合、右心房壁切除和中心分流手术在术后第13天成功使他脱离了呼吸机。患儿8个月大时进行腔肺吻合术,过程顺利。

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