Piotrowski W
Wiad Lek. 1997;50(7-9):222-5.
Congenital hip ectopy of one flat kidney is an excessively seldom developmental anomaly considering abnormal shape and ectopy with agenesia of one kidney. However, in literature, the kidney malformations are described very well, especially the ectopy of one of the kidneys and two-sided agenesia, but the presented case is exceptionally seldom anomaly. That is why it should be shown in the context of other defects of urinary tract. Abnormalities of urinary tract are the most often congenital defects among children. For example, two-sided agenesia occurs in 1, per 4800 live born children, while one-sided at 1:2500 to 1:2800. This defect occurs more often among boys 1.8:1 and on the left side 1.5:1. The tendency of family heredity was also noticed. Structural changes of right-sided ureteric bud accompany the defect very often. Usually it is an asymptomatic defect but in 50% girls and 10%-15% boys, other congenital defects occur together with this one. The lack of homonymous suprarenal gland, spermatic cord seminal vesicles and right testicle in boys is the most often accompanying anomaly. Organogenesis disorders connected with organs developing from Muller's tract are seen in girls.
先天性髋关节异位合并一侧扁平肾是一种极为罕见的发育异常，涉及肾脏形态异常、异位以及一侧肾发育不全。然而，在文献中，肾脏畸形已有详尽描述，尤其是一侧肾脏异位和双侧肾发育不全，但本病例所呈现的异常极为罕见。正因如此，应将其置于泌尿系统其他缺陷的背景下展示。泌尿系统异常是儿童中最常见的先天性缺陷。例如，双侧肾发育不全在每4800例活产儿中出现1例，而单侧肾发育不全的发生率为1:2500至1:2800。这种缺陷在男孩中更为常见，男女比例为1.8:1，且左侧更为多见，左右比例为1.5:1。同时也注意到了家族遗传倾向。右侧输尿管芽的结构改变常常伴随这种缺陷。通常这是一种无症状的缺陷，但在50%的女孩和10% - 15%的男孩中，会伴有其他先天性缺陷。男孩中同侧肾上腺、精索精囊和右侧睾丸缺失是最常见的伴随异常。女孩则可见与苗勒管发育器官相关的器官发生障碍。
