Rosenbaum J T, Roman-Goldstein S, Lindquist G R, Rosenbaum R B
School of Medicine, Casey Eye Institute, Oregon Health Sciences University, Portland 97201, USA.
J Rheumatol. 1998 Mar;25(3):593-7.
Vasculitis confined to the central nervous system (CNS) is a rare disease usually characterized by headache and focal neurologic symptoms. Patients with primary vasculitis of the CNS may have symptoms and laboratory findings of systemic disease such as fatigue and elevated erythrocyte sedimentation rate, but by definition, focal inflammation should not be present outside the CNS. We describe 3 patients with uveitis in association with this diagnosis. The recognition of this association adds to the complex differential diagnosis of uveitis in association with CNS disease, and indicates that "isolated" angiitis of the CNS may display clinical features outside the brain and spinal cord.
局限于中枢神经系统（CNS）的血管炎是一种罕见疾病，通常以头痛和局灶性神经症状为特征。中枢神经系统原发性血管炎患者可能有全身疾病的症状和实验室检查结果，如疲劳和红细胞沉降率升高，但根据定义，中枢神经系统以外不应存在局灶性炎症。我们描述了3例与该诊断相关的葡萄膜炎患者。认识到这种关联增加了与中枢神经系统疾病相关的葡萄膜炎复杂的鉴别诊断，并表明中枢神经系统“孤立性”血管炎可能在脑和脊髓之外表现出临床特征。
