[Congenital nystagmus with sensory disorder: reaction to the caloric and optokinetic stimulation].

The purpose of this study was to estimate the response on vestibular caloric and optokinetic stimulation in patients with congenital nystagmus and serious congenital anomalies of visual system. 58 patients, aged 11-20 (21 female, 37 male) underwent this stimulation with ENG registration. The patients had visual acuity from 0.04 to 0.4, caused by visual system diseases e.g. congenital cataract, optic atrophy, hypoplasia maculae, high refractive error, albinism ect. The correct response was observed with 15.5% of the patients on vestibular caloric stimulation. There was no statistically significant relationship between visual acuity or visual system disease and the correct response. 28% of the patients responded correctly on optokinetic stimulation. There was statistically significant relationship between visual system anomaly and correct OKN: 80% of this reaction was in the group of optic atrophy, 54% in the group of high refractive error. Statistically significant relationship was no observed between visual acuiy and correct OKN. High level of the incorrect response on the caloric and optokinetic stimulation in the persons with congenital nystagmus and congenital disorder of visual system limits using of this tests for diagnostic purpose.