Priscu V, Lurie S, Savir I, Rabinerson D, Hagay Z
Department of Anesthesia, Kaplan Hospital, Rehovot, Israel.
J Clin Anesth. 1998 Mar;10(2):153-5. doi: 10.1016/s0952-8180(97)00225-0.
Segawa's syndrome is a rare hereditary progressive dystonia with diurnal fluctuation, which, in contrast to other types of chronic dystonia in children, responds dramatically to levodopa therapy. We present a case of a patient, suffering from Segawa's syndrome who underwent two cesarean sections, and we describe our experience in providing anesthesia to that patient. The first cesarean section was performed with general anesthesia, while the second was accomplished with epidural anesthesia. On both occasions the anesthesia was uneventful.
Segawa综合征是一种罕见的遗传性进行性肌张力障碍，具有日波动现象，与儿童其他类型的慢性肌张力障碍不同，它对左旋多巴治疗反应显著。我们报告一例患有Segawa综合征的患者接受了两次剖宫产手术，并描述了为该患者提供麻醉的经验。第一次剖宫产采用全身麻醉，第二次采用硬膜外麻醉。两次麻醉过程均顺利。
